Vertebral aspergillosis in a patient with autosomal-dominant hyper-IgE syndrome.
نویسندگان
چکیده
We present a report of an autosomal-dominant hyper-IgE syndrome patient with vertebral aspergillosis. Early diagnosis and antifungal therapy with surgery are crucial for improving the outcome of this aggressive condition.
منابع مشابه
The hyperimmunoglobulin E syndrome - clinical manifestation diversity in primary immune deficiency
The hyper-IgE syndromes are rare, complex primary immunodeficiencies characterized by clinical manifestation diversity, by particular susceptibility to staphylococcal and mycotic infections as well as by a heterogeneous genetic origin. Two distinct entities--the classical hyper-IgE syndrome which is inherited in an autosomal dominant pattern and the autosomal recessive hyper-IgE syndrome--have ...
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عنوان ژورنال:
- Clinical and vaccine immunology : CVI
دوره 21 1 شماره
صفحات -
تاریخ انتشار 2014